Langerhan’s cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report

  • Suresh Mani Department of ENT, Christian Medical College, Vellore, India
  • Regi Thomas Department of ENT, Christian Medical College, Vellore, India
  • John Mathew Department of ENT, Christian Medical College, Vellore, India
  • Rajiv Michael Department of ENT, Christian Medical College, Vellore, India
Keywords: : blindness; histiocytosis; langerhans-cell; sphenoid sinus.

Abstract

Langerhan's cell histiocytosis is an uncontrolled proliferation of dendritic cells. The involvement of skull base is rare. Variable clinical presentation and multi organ involvement often warrant a multidisciplinary approach for a successful diagnosis. We are reporting a case of 16-year-old male with sphenoid sinus Langerhan’s cell histiocytosis which presented as a sudden and painless loss of vision. It is a rare entity in the diagnosis of blindness. Delayed diagnosis and treatment can result in serious complications. The radiological features and management options are discussed with a review of the pertinent literature.

 

Published
2019-08-31
How to Cite
Mani, S., Thomas, R., Mathew, J., & Michael, R. (2019). Langerhan’s cell Histiocytosis of Sphenoid Sinus causing Vision Loss: A Case Report. Journal of Nepal Medical Association, 57(218). https://doi.org/10.31729/jnma.3959
Section
Case Reports